Anatomically corrected malposition of great arteries
نویسندگان
چکیده
Anatomically corrected malposition of great arteries (ACMGA) is a rare form of congenital heart disease in which the great arteries arise above the anatomically correct ventricles but have abnormal spatial relationship. We report the case of a 26-year-old female with ACMGA and tunnel type of subaortic obstruction. The abnormal relationship and segmental arrangement necessitates systematic approach in evaluation for proper diagnosis and surgical repair. This unusual case is reported for its rarity and to highlight the need for awareness to differentiate it from other more common conditions.
منابع مشابه
[A case of intracardiac repair for anatomically corrected malposition of the great arteries (S, D, L)].
A 5-year-old boy with anatomically corrected malposition of the great arteries (Van Praah's {S, D, L} arrangement type) associated with ventricular septal defect (malalignment conus type) and pulmonary stenosis underwent a biventricular repair. Subpulmonary stenosis was repaired by muscle resection of narrowing muscular subpulmonary conus through the right ventricle. The postoperative catheteri...
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Anatomically corrected malposition of the great arteries is a congenital cardiac malformation in which the atria and ventricles are in concordant relation, as are the ventricles and great arteries, but the aorta is to the left of the pulmonary artery (1-position). The reported cases and our two patients have had situs solitus of viscera and atria. The aortic and pulmonary circulations are in se...
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Anatomically corrected malposition of the great arteries (ACMGA) is defined as parallel arising of aorta and main pulmonary artery (PA) roots although ventriculoarterial connection is normal. Abnormally related aorta arises from the left ventricle, while abnormally related PA arises from the right ventricle. It can be diagnosed with via echocardiography. In some cases, additional imaging modali...
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